Abdelbar Abdelrahman, Mahadevan Vaikom S, Austin Conal, Hoschtitzky J Andreas
Northwest Adult Congenital Heart Disease Unit, Manchester Heart Centre, Central Manchester Foundation Trust, Oxford Road, Manchester, United Kingdom.
World J Pediatr Congenit Heart Surg. 2013 Oct;4(4):444-6. doi: 10.1177/2150135113485759.
We report the case of a 54-year-old patient with complex univentricular physiology who presented with worsening exercise intolerance, chronic cyanosis, and uncontrolled heart failure. Investigations included echocardiography, cardiac magnetic resonance imaging, and cardiac catheterization. After discussion in a multidisciplinary meeting, the patient underwent successful surgery that included a bidirectional Glenn anastomosis and repair of the atrioventricular (AV) junction. She recovered well and on follow-up had substantially less cyanosis and heart failure. We demonstrated that common AV valve repair and Glenn shunt can be used together successfully in appropriately selected older patients as palliation for complex congenital heart disease with functionally univentricular physiology.
我们报告了一例54岁患有复杂单心室生理状况的患者，该患者出现运动耐量下降、慢性紫绀和心力衰竭控制不佳的症状。检查包括超声心动图、心脏磁共振成像和心导管检查。在多学科会议讨论后，该患者接受了成功的手术，包括双向格林吻合术和房室（AV）连接修复。她恢复良好，随访时紫绀和心力衰竭明显减轻。我们证明，对于功能上单心室生理状况的复杂先天性心脏病患者，在适当选择的老年患者中，共同进行房室瓣修复和格林分流术可成功用于姑息治疗。
