Georgekutty Justin, Cross Russell R, Rosenthal Joanna B, Heath Deneen M, Sinha Pranava, John Anitha S
1 Department of Pediatrics, Division of Cardiology, Children's National Medical Center, George Washington University, Washington, District of Columbia, United States of America.
2 Department of Pediatrics, Division of Cardiac Surgery, Children's National Medical Center, George Washington University, Washington, District of Columbia, United States of America.
Cardiol Young. 2014 Jun;24(3):397-402. doi: 10.1017/S1047951113002217. Epub 2013 Dec 17.
In the United States, hypertrophic cardiomyopathy and coronary artery anomalies account for the leading two causes of sudden death in athletes. We present a case of a patient with an anomalous origin of the left main from the right coronary sinus with associated gene-confirmed hypertrophic cardiomyopathy. The patient underwent surgical repair with unroofing of the intramural portion of the left main coronary artery with a good result. We also review the reported cases in the medical literature describing this uncommon association between anomalous coronary artery origin and hypertrophic cardiomyopathy.
在美国,肥厚型心肌病和冠状动脉异常是运动员猝死的两大主要原因。我们报告一例患者,其左主干起源于右冠状动脉窦并伴有基因确诊的肥厚型心肌病。该患者接受了手术修复,即对左主干冠状动脉壁内部分进行开窗,效果良好。我们还回顾了医学文献中报道的描述冠状动脉起源异常与肥厚型心肌病这种罕见关联的病例。