Segatto Majoriê Mergen, Schmitt Eloísa Unfer, Hagemann Laura Netto, Silva Roberta Castilhos da, Cattani Cristiane Almeida Soares
Federal University for Health Sciences, Porto AlegreRS, Brazil.
Sanitary Dermatology Outpatient Clinic, Porto AlegreRS, Brazil.
An Bras Dermatol. 2013 Nov-Dec;88(6 Suppl 1):85-8. doi: 10.1590/abd1806-4841.20132248.
Phacomatosis Pigmentovascularis is a rare syndrome characterized by capillary malformation and pigmentary nevus. A case of a 2-year-old patient is reported, who presented extensive nevus flammeus and an aberrant Mongolian spot, without systemic disease, manifestations that allow us to classify this case as type IIa Phacomatosis Pigmentovascularis, according to Hasegawa's classification.
色素血管性斑痣性错构瘤病是一种以毛细血管畸形和色素痣为特征的罕见综合征。本文报道了1例2岁患者,该患者有广泛的鲜红斑痣和异常蒙古斑,无全身疾病,根据长谷川分类,这些表现使我们将该病例归类为色素血管性斑痣性错构瘤病IIa型。