Pacheco Luiz Frederico, Fernandes Bruno F, Miyamoto Cristina, Maloney Shawn C, Arthurs Bryan, Burnier Miguel N
Department of Ophthalmology, McGill University Health Center, Montreal, QC, Canada ; Faculty of Medicine, Federal University of Rio de Janeiro, Rio De Janeiro, Brazil.
Department of Ophthalmology, McGill University Health Center, Montreal, QC, Canada.
Clin Ophthalmol. 2014;8:31-3. doi: 10.2147/OPTH.S47901. Epub 2013 Dec 10.
Hemangiopericytoma is a rare vascular tumor that originates from pericytes. The orbit is a rare location for this particular tumor, and corresponds to 0.8% to 3% of all primary orbital tumors. We report a case of a hemangiopericytoma in a 45-year-old man that had an unusual presentation, as a rapidly growing mass in the anterior right inferior orbit. Given that there are no clinical or radiological signs pathognomonic of this tumor, a careful histopathological examination is necessary to confirm the diagnosis. In our case, it presented also with unusual histopathological findings. The clinical features, radiological findings, differential diagnosis and treatment of this challenging entity are reviewed in this case report.
血管外皮细胞瘤是一种起源于周细胞的罕见血管肿瘤。眼眶是这种特殊肿瘤的罕见发病部位，占所有原发性眼眶肿瘤的0.8%至3%。我们报告了一例45岁男性的血管外皮细胞瘤，其表现不寻常，为右眼下前部眼眶迅速生长的肿块。鉴于该肿瘤没有特异性的临床或放射学征象，因此需要仔细的组织病理学检查来确诊。在我们的病例中，还呈现出不寻常的组织病理学表现。本病例报告对这个具有挑战性的疾病的临床特征、放射学表现、鉴别诊断及治疗进行了综述。
