From the Medical College of Georgia, Georgia Regents University, Augusta.
Neurology. 2014 Feb 11;82(6):540-2. doi: 10.1212/WNL.0000000000000100. Epub 2014 Jan 2.
Immunoglobulin G4-related diseases (IgG4-RD) are a newly recognized category of diseases. CNS involvement in IgG4-RD includes hypophysitis(1) and intracranial or spinal manifestations of hypertrophic pachymeningitis.(2,3) We present a unique case of rapid cognitive decline due to IgG4-related leptomeningitis.
免疫球蛋白 G4 相关疾病(IgG4-RD)是一种新认识的疾病类别。CNS 受累的 IgG4-RD 包括垂体炎(1)和肥厚性脑膜脑炎的颅内或脊髓表现。(2,3)我们报告了一例因 IgG4 相关软脑膜炎导致认知功能迅速下降的独特病例。