贝切特病伴三体 8 骨髓增生异常综合征：两例报告并复习 15 例日本病例。
Behçet's disease accompanied by myelodysplastic syndrome with trisomy 8: two case reports and a review of 15 Japanese cases.
机构信息
Division of Rheumatology, Department of Internal Medicine, Institute of Clinical Medicine, University of Tsukuba , 1-1-1 Tennodai, Tsukuba 305-8575 , Japan.
出版信息
Mod Rheumatol. 2003 Mar;13(1):90-4. doi: 10.3109/s101650300015.
Abstract We describe two cases of Behçet's disease associated with myelodysplastic syndrome (MDS) with trisomy 8. Both cases developed ulceration in the cecum as a gastrointestinal complication of Behçet's disease, after a diagnosis of MDS. We summarized recent case reports of Behçet's disease associated with myelodysplastic syndrome, and studied the clinical manifestations. Most cases showed trisomy 8 as a chromosomal abnormality. Gastrointestinal involvement without eye lesions seems to be characteristic of Behçet's disease associated with MDS.
摘要
我们描述了两例骨髓增生异常综合征（MDS）伴 8 号三体的贝赫切特病（Behçet's disease）病例。这两例患者在 MDS 确诊后，均以胃肠道并发症的形式出现盲肠溃疡。我们对骨髓增生异常综合征伴发贝赫切特病的近期病例报告进行了总结，并研究了其临床表现。大多数病例表现为 8 号三体的染色体异常。无眼部病变的胃肠道受累似乎是 MDS 伴发贝赫切特病的特征。
Zotero 插件