Paronen Johanna, Väisänen Mika, Leijon Helena
HYKS, Jorvin sairaala, medisiininen tulosyksikkö, endokrinologian klinikka.
HYKS, Jorvin sairaala, operatiivinen tulosyksikkö, vatsaelinkirurgian klinikka.
Duodecim. 2013;129(22):2375-8.
Pheochromocytoma is a tumor of the chromaffin tissue, originating from the suprarenal medulla and secreting cathecolamines, adrenalin and noradrenalin. Because the symptoms of this rare disease may deceptively resemble those of other diseases, its diagnosis may be delayed. Episodic symptoms are characteristic of pheochromocytoma. In most cases the tumor is curable with surgery, but untreated may lead to sudden death of the patient, or have time to spread. Alpha-blockade is started before the operation. The operations should be concentrated to units specialized in endocrine surgery.
嗜铬细胞瘤是一种起源于肾上腺髓质、分泌儿茶酚胺、肾上腺素和去甲肾上腺素的嗜铬组织肿瘤。由于这种罕见疾病的症状可能会令人误解地类似于其他疾病的症状，其诊断可能会延迟。发作性症状是嗜铬细胞瘤的特征。在大多数情况下，肿瘤可通过手术治愈，但如果不治疗可能导致患者猝死，或者有时间扩散。手术前开始使用α受体阻滞剂。手术应集中在专门从事内分泌外科的单位进行。
