Shin Yu Seob, Kim Hyung Jin, Kim Myung Ki
Department of Urology, Chonbuk National University Medical School, and Research Institute of Clinical Medicine of Chonbuk National University-Biomedical Research Institute of Chonbuk National University Hospital, Jeonju, South Korea.
Can Urol Assoc J. 2013 Sep-Oct;7(9-10):E657-9. doi: 10.5489/cuaj.1217.
Juxta-adrenal malignant schwannoma is a very rare tumour of neural crest cell origin. A 69-year-old woman visited for proper management of incidentally detected adrenal mass as part of a dyspepsia workup. Metabolic evaluation was unremarkable and imaging results suggested a malignant adrenal mass with lymph node metastases. The patient underwent a left adrenalectomy with para-aortic lymphadenectomy. The diagnosis and its origin was confirmed by histologic and immunohistochemical studies. We report the first case of juxta-adrenal malignant schwannoma with lymph node metastases, and review the literature on this rare tumour.
肾上腺旁恶性神经鞘瘤是一种非常罕见的起源于神经嵴细胞的肿瘤。一名69岁女性因消化不良检查偶然发现肾上腺肿块前来寻求恰当治疗。代谢评估无异常,影像学结果提示为肾上腺恶性肿块伴淋巴结转移。患者接受了左肾上腺切除术及腹主动脉旁淋巴结清扫术。组织学和免疫组化研究证实了诊断及其起源。我们报告首例肾上腺旁恶性神经鞘瘤伴淋巴结转移的病例,并对有关这种罕见肿瘤的文献进行综述。