帕里-罗姆伯格综合征：一例罕见病例报告。
Parry-romberg syndrome: a rare case report.
作者信息
Rangare Anusha Laxman, Babu Subhas Gogineni, Thomas Priya Sara, Shetty Shishir Ram
机构信息
Department of Oral and Maxillofacial Radiology, AB Shetty Memorial Institute of Dental Sciences, Nitte University Deralakatte, Mangalore, Karnataka India.
出版信息
J Oral Maxillofac Res. 2011 Jul 1;2(2):e5. doi: 10.5037/jomr.2011.2205. eCollection 2011.
BACKGROUND
The purpose of this report is to present a rare entity of Parry-Romberg syndrome. This poorly understood degenerative condition is characterised by atrophic changes affecting one side of the face. The cause of these changes remains obscure.
METHODS
The authors report one rare case of a 31 year old female patient with Parry-Romberg syndrome, accompanied by a brief review of literature.
RESULTS
Clinical examination of the patient revealed evident facial asymmetry, malar hypoplasia, atrophy of skin and other tissues on the left side, hyperpigmentation of skin on the left side of the face. Final diagnosis of a Parry-Romberg syndrome ("progressive hemifacial atrophy") was based on thorough clinical and a radiological examination. Treatment using alloplastic implants to improve facial disfigurement was suggested to the patient.
CONCLUSIONS
In most cases, Parry-Romberg syndrome appears to occur randomly for unknown reasons. The pathophysiology of the syndrome remains unknown. There is no definitive treatment for this condition but an attempt to use restorative plastic surgery which includes fat or silicone implants, flap/pedicle grafts, or bone implants can be done to improve facial disfigurement.
背景
本报告旨在介绍一种罕见的帕里-罗姆伯格综合征病例。这种了解甚少的退行性疾病的特征是面部一侧出现萎缩性变化。这些变化的原因仍不明确。
方法
作者报告了一例31岁女性帕里-罗姆伯格综合征患者的罕见病例，并对相关文献进行了简要回顾。
结果
对该患者的临床检查发现明显的面部不对称、颧骨发育不全、左侧皮肤及其他组织萎缩、面部左侧皮肤色素沉着。基于全面的临床和放射学检查，最终诊断为帕里-罗姆伯格综合征（“进行性半侧面部萎缩”）。建议患者采用异体植入物治疗以改善面部畸形。
结论
在大多数情况下，帕里-罗姆伯格综合征似乎因不明原因随机发生。该综合征的病理生理学仍不清楚。这种疾病没有确切的治疗方法，但可以尝试采用修复性整形手术，包括脂肪或硅胶植入、皮瓣/带蒂移植或骨植入，以改善面部畸形。
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