Haldar Amit, Mukherjee Arabinda
Department of Neurology, Vivekananda Institute of Medical Sciences and Ramkrishna Mission Seva Pratisthan, Sarat Bose Road, Kolkata, India.
Neurol India. 2007 Apr-Jun;55(2):160-2. doi: 10.4103/0028-3886.32791.
Parry Romberg's syndrome is an uncommon disorder characterized by atrophy of skin and subcutaneous tissue of one side of face. It has neurologic sequel. The commonest of which is epilepsy. Here, we present a 17-year old girl with features of Parry Romberg's disease with intractable epilepsy. Her seizures have stopped with systemic corticosteroids. This treatment response, together with previous reports is suggestive of an autoimmune basis to this disorder. Thus the epilepsy in some such cases may be steroid responsive.
帕里-龙贝格综合征是一种罕见的疾病，其特征为一侧面部皮肤和皮下组织萎缩。它有神经学后遗症，其中最常见的是癫痫。在此，我们报告一名17岁患有帕里-龙贝格病且伴有难治性癫痫的女孩。她的癫痫发作通过全身使用皮质类固醇后已停止。这种治疗反应以及先前的报告提示该疾病存在自身免疫基础。因此，某些此类病例中的癫痫可能对类固醇有反应。
