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The molecular and biochemical basis of cystic fibrosis.

作者信息

McPherson M A, Dormer R L

机构信息

Department of Medical Biochemistry, University of Wales College of Medicine, Heath Park, Cardiff, UK.

出版信息

Biosci Rep. 1987 Mar;7(3):167-85. doi: 10.1007/BF01124787.

DOI:10.1007/BF01124787
PMID:2444282
Abstract
摘要

相似文献

1
The molecular and biochemical basis of cystic fibrosis.囊性纤维化的分子与生化基础。
Biosci Rep. 1987 Mar;7(3):167-85. doi: 10.1007/BF01124787.
2
Defective regulation of apical membrane chloride transport and exocytosis in cystic fibrosis.囊性纤维化中顶端膜氯离子转运和胞吐作用的调节缺陷。
Biosci Rep. 1988 Feb;8(1):27-33. doi: 10.1007/BF01128969.
3
Molecular and cellular biology of cystic fibrosis.囊性纤维化的分子与细胞生物学
Mol Aspects Med. 1991;12(1):1-81. doi: 10.1016/0098-2997(91)90015-e.
4
Theories of the pathogenesis of cystic fibrosis.囊性纤维化的发病机制理论。
Postgrad Med. 1971 Oct;50(4):92-7. doi: 10.1080/00325481.1971.11697630.
5
Fluid transport across cultures of human tracheal glands is altered in cystic fibrosis.在囊性纤维化中，跨人类气管腺培养物的液体转运发生改变。
J Physiol. 1997 Jun 15;501 ( Pt 3)(Pt 3):637-47. doi: 10.1111/j.1469-7793.1997.637bm.x.
6
Chloride and fluid secretion in polycystic kidney disease.多囊肾病中的氯离子与液体分泌
J Am Soc Nephrol. 1998 May;9(5):903-16. doi: 10.1681/ASN.V95903.
7
Acid in the airways. Focus on "Hyperacidity of secreted fluid from submucosal glands in early cystic fibrosis".气道中的酸。聚焦于“早期囊性纤维化时黏膜下腺分泌液的胃酸过多”。
Am J Physiol Cell Physiol. 2006 Mar;290(3):C669-71. doi: 10.1152/ajpcell.00525.2005.
8
The pathogenesis of cystic fibrosis: a proposal for calmodulin as the basic biochemical defect.
Med Hypotheses. 1986 Jul;20(3):245-53. doi: 10.1016/0306-9877(86)90040-x.
9
Chloride and potassium channels in cystic fibrosis airway epithelia.囊性纤维化气道上皮细胞中的氯离子和钾离子通道
Nature. 1986;322(6078):467-70. doi: 10.1038/322467a0.
10
Biochemical and genetic exclusion of calmodulin as the site of the basic defect in cystic fibrosis.钙调蛋白作为囊性纤维化基本缺陷位点的生化与遗传学排除研究
Hum Genet. 1987 Jul;76(3):278-82. doi: 10.1007/BF00283623.

引用本文的文献

1
Recent advances in cystic fibrosis.囊性纤维化的最新进展
J Inherit Metab Dis. 1988;11 Suppl 1:94-109. doi: 10.1007/BF01800575.
2
Influence of the glomerular filtration rate on renal clearance of ceftazidime in cystic fibrosis.肾小球滤过率对囊性纤维化患者头孢他啶肾清除率的影响。
Clin Pharmacokinet. 1988 Jul;15(1):57-65. doi: 10.2165/00003088-198815010-00005.
3
Cl- permeability of human sweat duct cells monitored with fluorescence-digital imaging microscopy: evidence for reduced plasma membrane Cl- permeability in cystic fibrosis.
用荧光数字成像显微镜监测人汗腺导管细胞的氯离子通透性：囊性纤维化中质膜氯离子通透性降低的证据。
Proc Natl Acad Sci U S A. 1989 Dec;86(24):10166-70. doi: 10.1073/pnas.86.24.10166.
4
Defective phosphorylation of a calmodulin-binding protein in cystic-fibrosis submandibular glands.囊性纤维化患者下颌下腺中钙调蛋白结合蛋白磷酸化缺陷
Biochem J. 1989 Oct 15;263(2):613-6. doi: 10.1042/bj2630613.
5
High osmolarity is a signal for enhanced algD transcription in mucoid and nonmucoid Pseudomonas aeruginosa strains.高渗透压是黏液型和非黏液型铜绿假单胞菌菌株中algD转录增强的信号。
J Bacteriol. 1989 May;171(5):2312-7. doi: 10.1128/jb.171.5.2312-2317.1989.
6
Increased renal clearance of cefsulodin due to higher glomerular filtration rate in cystic fibrosis.由于囊性纤维化患者肾小球滤过率较高，头孢磺啶的肾脏清除率增加。
Clin Pharmacokinet. 1990 Feb;18(2):168-75. doi: 10.2165/00003088-199018020-00006.
7
Chloride transport in cultured nasal epithelium of cystic fibrosis patients.
Pflugers Arch. 1990 Feb;415(5):540-6. doi: 10.1007/BF02583504.
8
Mucinophilic and chemotactic properties of Pseudomonas aeruginosa in relation to pulmonary colonization in cystic fibrosis.铜绿假单胞菌的嗜黏蛋白及趋化特性与囊性纤维化患者肺部定植的关系
Infect Immun. 1990 Jun;58(6):1489-95. doi: 10.1128/iai.58.6.1489-1495.1990.
9
Alginate synthesis by Pseudomonas aeruginosa: a key pathogenic factor in chronic pulmonary infections of cystic fibrosis patients.铜绿假单胞菌合成藻酸盐：囊性纤维化患者慢性肺部感染的关键致病因素。
Clin Microbiol Rev. 1991 Apr;4(2):191-206. doi: 10.1128/CMR.4.2.191.