Khaja Faseeh, Carilli Allison, Baidas Said, Sriharan Aravindhan, Norford Shanedelle
Division of Hematology/Oncology, MD Anderson Cancer Center Orlando, 1400 South Orange, MP 700, Orlando, FL 32806, USA.
Pathology Department, Orlando Health, 1414 Kuhl Avenue, Orlando, FL 32806, USA.
Case Rep Med. 2013;2013:904126. doi: 10.1155/2013/904126. Epub 2013 Dec 29.
Perivascular epithelioid cell tumors are soft tissue tumors that can occur in various locations in the body whose incidence is rising. Hepatic PEComas are quite rare and diagnosis involves positivity of Melan-A and HMB45 on immunohistochemistry. Usual treatment is surgery for benign tumors and chemotherapy including mTOR inhibitors for malignant tumors. Here we discuss the radiological and pathological diagnosis, evaluation, and management of a hepatic PEComa. We describe a 51-year-old patient who was diagnosed incidentally after unusual physical exam findings.
血管周上皮样细胞肿瘤是一种软组织肿瘤,可发生于身体的各个部位,其发病率正在上升。肝血管周上皮样细胞瘤相当罕见,诊断需要免疫组化检测Melan-A和HMB45呈阳性。良性肿瘤通常采用手术治疗,恶性肿瘤则采用包括mTOR抑制剂在内的化疗。在此,我们讨论一例肝血管周上皮样细胞瘤的放射学和病理学诊断、评估及治疗。我们描述了一名51岁的患者,其在体格检查发现异常后被偶然诊断。