Lorenzon Laura, Ziparo Vincenzo, Caterino Salvatore, Vecchione Andrea, Camboni Alessandra, Cavallini Marco
Ann Ital Chir. 2013 Nov-Dec;84(6):693-7.
Cavernous hemangiomas are rare tumors, mainly localized in the liver and skin, but also reported in the cerebellum and eye fundus as a part of von Hippel Lindau Syndrome. Adrenal hemangiomas are less than 1% of all the adrenal neoplasms and usually are reported as benign, non-functioning tumors, originating from the adrenal cortex and surrounded by normal or hyperplastic adrenal tissue.
We report the case of patient with bilateral hemangiomas of the adrenal glands associated with a subclinical hypercortisolism, incidentally detected during the pre-operative staging evaluation of a right colon cancer.
To the best of our knowledge, this is the third bilateral adrenal hemangioma ever reported case, the first one treated with surgical resection (right adrenalectomy and surgical resection of the left adrenal mass, sparing the left adrenal gland below). Pathogenesis, presentation and management of this rare neoplasm are here reviewed and discussed.
海绵状血管瘤是罕见肿瘤,主要位于肝脏和皮肤,但也有报道称其作为冯·希佩尔-林道综合征的一部分出现在小脑和眼底。肾上腺血管瘤占所有肾上腺肿瘤的比例不到1%,通常被报道为起源于肾上腺皮质、被正常或增生的肾上腺组织包围的良性无功能肿瘤。
我们报告了一例双侧肾上腺血管瘤患者,该患者伴有亚临床皮质醇增多症,在右结肠癌术前分期评估期间偶然发现。
据我们所知,这是第三例双侧肾上腺血管瘤报告病例,第一例采用手术切除治疗(右肾上腺切除术和左肾上腺肿块手术切除,保留下方的左肾上腺)。本文对这种罕见肿瘤的发病机制、表现和治疗进行了回顾和讨论。