Enuh Hilary A, Arsura Edward L, Cohen Zaza, Diaz Keith T, Nfonoyim Jay M, Cosentino Phillip J, Saverimuttu Jessie K
Department of Internal Medicine, Richmond University Medical Center, Staten Island, NY, USA.
Pulmonary and Critical Care Medicine, Richmond University Medical Center, Staten Island, NY, USA.
Int Med Case Rep J. 2014 Mar 20;7:53-6. doi: 10.2147/IMCRJ.S54850. eCollection 2014.
Congenital cystic adenomatoid malformation, currently referred as congenital pulmonary airway malformation (CPAM), is one of the rare lung malformations seen in adults. We report a case of a 59-year-old male with a chronic cough and hemoptysis that was not amenable to bronchial embolization. Further work up revealed cystic changes with fungal ball and type 1 CPAM. Patients with this condition who survive to adulthood usually suffer from recurrent respiratory bacterial infections. Only three cases of fungal involvement have ever been described. We present a fatal case, as well as the oldest patient.
先天性囊性腺瘤样畸形,目前称为先天性肺气道畸形(CPAM),是成人中罕见的肺部畸形之一。我们报告一例59岁男性患者,患有慢性咳嗽和咯血,支气管栓塞治疗无效。进一步检查发现有囊性改变伴真菌球及1型CPAM。存活至成年的此类患者通常患有复发性呼吸道细菌感染。仅有3例真菌累及的病例曾被描述。我们呈现了一例致命病例以及年龄最大的患者。