一名22岁女性患累及全肺的囊性腺瘤样畸形。

Cystic adenomatoid malformation involving an entire lung in a 22-year-old woman.

作者信息

Lackner R P, Thompson A B, Rikkers L F, Galbraith T A

机构信息

Department of Surgery, University of Nebraska Medical Center, Omaha 68198-2315, USA.

出版信息

Ann Thorac Surg. 1996 Jun;61(6):1827-9. doi: 10.1016/0003-4975(95)01197-8.

DOI:10.1016/0003-4975(95)01197-8

PMID:8651796

Abstract

Congenital cystic adenomatoid malformation is an uncommon cause of respiratory distress in infants and is a rare entity in adults. Presentation in older patients is that of recurrent pulmonary infections. Usually a single lobe is involved. This report describes congenital cystic adenomatoid malformation involving the entire right lung in a 22-year-old woman presenting with gastrointestinal bleeding due to cavernous transformation of the portal and splenic veins.

摘要

先天性囊性腺瘤样畸形是婴儿呼吸窘迫的罕见病因，在成人中更是罕见。老年患者的表现为反复肺部感染。通常累及单个肺叶。本报告描述了一名22岁女性，因门静脉和脾静脉海绵样变导致胃肠道出血，其先天性囊性腺瘤样畸形累及整个右肺。