Gautam Munnangi Satya, Naren Satya Srinivas M, Prathyusha Ivvala Sai, Reddy K Hema Chandra, Mayilvaganan Kamala Retnam, Raidu Deepthi
Department of Radiodiagnosis, Jawaharlal Nehru Medical College, Belgaum, India.
Department of Radiodiagnosis, M.V. Jayaram Medical College and Research Hospital, Hosakote, Karnataka, India.
Pol J Radiol. 2017 Jun 4;82:299-303. doi: 10.12659/PJR.901447. eCollection 2017.
Congenital pulmonary airway malformation (CPAM) is a relatively rare congenital anomaly with a wide spectrum of ultrasound features depending on the specific variety of CPAM. Antenatal ultrasound is a valuable, safe, nonionizing, cost-effective, widely available and easily reproducible imaging tool and is indispensable in the diagnosis of CPAM. In this paper, we aimed to report an atypical imaging presentation of CPAM type II in the second trimester, extensively involving all lobes of the left lung.
A 25-year-old G1P0A0 woman with a gestational age of around 22 weeks was referred for an anomaly scan. The antenatal ultrasound scan showed a single, live, intrauterine foetus corresponding to a gestational age of around 22 weeks and 4 days. There were multiple, anechoic structures noted within the pulmonary tissue in the left hemithorax, each measuring around 3 to 4 mm in diameter. The lesion was extending from the left lower lobe up to the apical (apicoposterior) segment of the left upper lobe. The ultrasound diagnosis of congenital pulmonary airway malformation type II was made. After explaining the condition and the poor prognosis to the patient, an informed consent was obtained after she opted for medical termination of pregnancy.
Congenital pulmonary airway malformation (CPAM) is an uncommon foetal anomaly with a very wide range of ultrasound appearances depending on the specific type of CPAM. CPAM also has a wide spectrum of differential diagnoses and a variable prognosis. Antenatal ultrasound should always be the primary mode of diagnosis in CPAM.
先天性肺气道畸形（CPAM）是一种相对罕见的先天性异常，根据CPAM的具体类型，具有广泛的超声特征。产前超声是一种有价值、安全、非电离、经济高效、广泛可用且易于重复的成像工具，在CPAM的诊断中不可或缺。在本文中，我们旨在报告一例孕中期II型CPAM的非典型影像学表现，广泛累及左肺的所有肺叶。
一名25岁、孕1产0、无流产史的女性，孕周约22周，因异常扫描前来就诊。产前超声扫描显示一个单活胎，宫内胎儿孕周约为22周4天。左半胸肺组织内可见多个无回声结构，每个直径约3至4毫米。病变从左肺下叶延伸至左肺上叶尖段（尖后段）。超声诊断为II型先天性肺气道畸形。在向患者解释病情和不良预后后，患者选择终止妊娠并签署了知情同意书。
先天性肺气道畸形（CPAM）是一种罕见的胎儿异常，根据CPAM的具体类型，超声表现范围非常广泛。CPAM的鉴别诊断范围也很广，预后各不相同。产前超声应始终是CPAM诊断的主要方式。
