Budzynska Agnieszka, Hartleb Marek, Nowakowska-Dulawa Ewa, Krol Robert, Remiszewski Piotr, Mazurkiewicz Michal
Agnieszka Budzynska, Marek Hartleb, Ewa Nowakowska-Dulawa, Department of Gastroenterology and Hepatology, Medical University of Silesia, 40-752 Katowice, Poland.
World J Gastroenterol. 2014 Apr 14;20(14):4102-5. doi: 10.3748/wjg.v20.i14.4102.
Cystic hepatic neoplasms are rare tumors, and are classified into two separate entities: mucinous cystic neoplasms (MCNs) and intraductal papillary mucinous neoplasms of the bile duct (IPMN-B). We report the case of a 56-year-old woman who presented with abdominal pain and jaundice due to the presence of a large hepatic multilocular cystic tumor associated with an intraductal tumor. Partial hepatectomy with resection of extrahepatic bile ducts demonstrated an intrahepatic MCN and an intraductal IPMN-B. This is the first report of the simultaneous occurrence of these two histologically distinct entities in the liver.
肝囊性肿瘤是罕见肿瘤，可分为两个不同类型：黏液性囊性肿瘤（MCNs）和胆管内乳头状黏液性肿瘤（IPMN-B）。我们报告一例56岁女性病例，该患者因存在一个与肝外胆管内肿瘤相关的巨大肝脏多房性囊性肿瘤而出现腹痛和黄疸。行肝部分切除术并切除肝外胆管后发现为肝内MCN和胆管内IPMN-B。这是首次关于这两种组织学不同类型在肝脏同时发生的报告。
