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β地中海贫血骨髓外造血所致脊髓压迫性轻截瘫经紧急放射治疗后完全恢复

Complete recovery from paraparesis in spinal cord compression due to extramedullary haemopoiesis in beta-thalassaemia by emergency radiation therapy.

作者信息

Ruo Redda M G, Allis S, Reali A, Bartoncini S, Roggero S, Anglesio S M, Piga A

机构信息

Radiation Oncology Unit, Department of Oncology, S. Luigi Hospital, University of Turin, Orbassano, Italy.

出版信息

Intern Med J. 2014 Apr;44(4):409-12. doi: 10.1111/imj.12386.

Abstract

Extramedullary haemopoiesis (EMH) is a complication commonly associated with beta-thalassaemia intermedia; it is frequently asymptomatic but can sometimes lead to symptomatic tumour-like masses. No guidelines or common consensus are available in literature regarding the different treatment strategies and only single cases have been reported. We describe a case of spinal cord compression due to intrathoracic EMH masses treated with combined radiotherapy and hydroxyurea.

摘要

髓外造血(EMH)是一种常见于中间型β地中海贫血的并发症;它通常无症状,但有时可导致出现有症状的肿瘤样肿块。文献中没有关于不同治疗策略的指南或共识,仅有个别病例报道。我们描述了一例因胸段髓外造血肿块导致脊髓压迫的病例,该病例采用放疗联合羟基脲进行治疗。

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