Bakhshi Girish D, Khan Arshad S, Shaikh Aftab S, Khan Mohammad Ashraf A, Khan Mohammad Adil A, Jamadar Nilofar M
Department of Surgery and.
Department of Radiology, Grant Medical College & Sir J.J. Group of Hospitals, Mumbai, India.
Clin Pract. 2012 Mar 30;2(2):e44. doi: 10.4081/cp.2012.e44.
Primary Renal Sarcoma is rare tumor comprising only 1% of all renal tumours. Synovial sarcomas are generally deep-seated tumors arising in the proximity of large joints of adolescents and young adults and account for 5-10% of all soft tissue tumours. Primary synovial sarcoma of kidney is rare and has poor prognosis. It can only be diagnosed by immunohistochemistry. It should be considered as a differential in sarcomatoid and spindle cell tumours. We present a case of 33-year-old female, who underwent left sided radical nephrectomy for renal tumour. Histopathology and genetic analysis diagnosed it to be primary renal synovial sarcoma. Patient underwent radiation therapy and 2 years follow up is uneventful. A brief case report with review of literature is presented.
原发性肾肉瘤是一种罕见的肿瘤，仅占所有肾肿瘤的1%。滑膜肉瘤通常是深部肿瘤，发生于青少年和年轻成年人的大关节附近，占所有软组织肿瘤的5% - 10%。原发性肾滑膜肉瘤罕见且预后不良。它只能通过免疫组织化学诊断。在肉瘤样和梭形细胞瘤中应将其视为鉴别诊断。我们报告一例33岁女性，因肾肿瘤接受了左侧根治性肾切除术。组织病理学和基因分析诊断为原发性肾滑膜肉瘤。患者接受了放射治疗，2年随访情况良好。本文给出了一份简要病例报告并对文献进行了综述。
