Slater Rick C, Iheagwara Uzoma, Chen Mang L
University of Pittsburgh Medical Center, Pittsburgh, Pennsylvania, USA.
Can J Urol. 2014 Apr;21(2):7248-50.
Renal lymphangiomatosis is a disease characterized by abnormal formation of perirenal lymphatic vessels that fail to communicate with other retroperitoneal lymphatics; as a result, perirenal lymphatics dilate and form cysts. While typically an asymptomatic incidental finding, renal lymphangiomatosis rarely presents as flank or abdominal pain, ascites, impaired renal function, hypertension, hematuria, or proteinuria. Here we present the first known case of renal lymphangiomatosis found to spontaneously resolve following cardiac transplantation.
肾淋巴管瘤病是一种以肾周淋巴管异常形成且无法与其他腹膜后淋巴管相通为特征的疾病;结果,肾周淋巴管扩张并形成囊肿。虽然通常是无症状的偶然发现,但肾淋巴管瘤病很少表现为胁腹或腹痛、腹水、肾功能损害、高血压、血尿或蛋白尿。在此,我们报告首例已知的肾淋巴管瘤病病例,该病例在心脏移植后自发缓解。