Belsky Justin, Whitcomb Valerie, Zimmerman Eric, Stankovic Curt
From the *Henry Ford Health System; †Children's Hospital of Michigan; and ‡Detroit Medical Center, Detroit, MI.
Pediatr Emerg Care. 2014 May;30(5):352-3. doi: 10.1097/PEC.0000000000000129.
Rapunzel syndrome is defined as a gastric trichobezoar with a tail that extends distally into the small intestine. It is extremely rare and found more often in premenarchal girls with psychiatric comorbidities. Symptoms can be vague and linger for years. However, prolonged intake of indigestible material can lead to gastric outlet obstruction, which may present similarly to a small bowel obstruction. The standard imaging modality of choice to make a presurgical diagnosis is via computed tomography (CT) scan of the abdomen. However, the risk of radiation-induced malignancy associated with a CT scan is an important consideration when managing children. We report a case of Rapunzel syndrome in a 6-year-old girl who was diagnosed presurgically without the use of a CT scan.
长发公主综合征的定义是胃内毛发石伴有一条向远端延伸至小肠的尾巴。它极为罕见，更常见于患有精神疾病合并症的青春期前女孩。症状可能不明确且会持续数年。然而，长期摄入难以消化的物质会导致胃出口梗阻，其表现可能与小肠梗阻相似。术前诊断的标准影像学检查方法是腹部计算机断层扫描（CT）。然而，在处理儿童患者时，与CT扫描相关的辐射诱发恶性肿瘤风险是一个重要的考虑因素。我们报告了一例6岁女孩的长发公主综合征病例，该病例在未使用CT扫描的情况下进行了术前诊断。
