Department of Cardiovascular Surgery, Sakakibara Heart Institute, Tokyo, Japan.
Department of Cardiovascular Surgery, Sakakibara Heart Institute, Tokyo, Japan.
Ann Thorac Surg. 2014 May;97(5):1786-8. doi: 10.1016/j.athoracsur.2013.08.022.
Type IV Ehlers-Danlos syndrome is a life-threatening inherited disorder of connective tissue associated with multiple aneurysm formation. Thoracoabdominal aortic repair in these patients has rarely been performed. We report the case of a 13-year-old patient with Ehlers-Danlos syndrome who had multiple aortic operations from the ascending aorta to the thoracoabdominal aorta.
IV 型埃勒斯-当洛斯综合征是一种危及生命的遗传性结缔组织疾病，与多种动脉瘤形成有关。这些患者的胸主动脉-腹主动脉修复很少进行。我们报告了一例 13 岁的埃勒斯-当洛斯综合征患者，他曾多次接受从升主动脉到胸主动脉-腹主动脉的主动脉手术。
