Singh Adarshlata, Singhal Kritika, Choudhary Sanjiv, Bisati Shazia, Arora Mallika
Department of Dermatology, Venereology, and Leprosy, Jawaharlal Nehru Medical College, Datta Meghe Institute of Medical Sciences (Deemed University), Sawangi (Meghe), Wardha, Maharashtra, India.
Indian J Dermatol. 2014 May;59(3):316. doi: 10.4103/0019-5154.131459.
Disabling pansclerotic morphea (DPM) is a rare, severe, and mutilating form of morphea, involving the dermis, subcutaneous tissue, fat, muscle, and even bone. It is usually seen before the age of 14 years, with the patient complaining of arthralgia and stiffness at the time of onset. We report a case of unilateral adult-onset DPM with sparing of the face. Within a few months of onset, painful contracture deformities of the hand, elbow, and shoulder joints developed, impairing the patient's normal daily activities. We are reporting this case because of the unusual presentation: DPM in an adult, with history of trauma in childhood and rapid onset of complications, is rare.
致残性全硬化性硬斑病（DPM）是硬斑病的一种罕见、严重且致残的形式，累及真皮、皮下组织、脂肪、肌肉甚至骨骼。它通常在14岁之前出现，患者在发病时会抱怨关节痛和僵硬。我们报告一例单侧成人发病的DPM，面部未受累。发病后几个月内，手部、肘部和肩关节出现疼痛性挛缩畸形，影响了患者的正常日常活动。我们报告这个病例是因为其表现不寻常：成人发生的DPM，有童年创伤史且并发症迅速出现，这种情况很罕见。
