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镰状细胞贫血青少年双侧重度感音神经性听力损失的人工耳蜗植入

Cochlear implant for bilateral profound sensorineural hearing loss in an adolescent with sickle cell anemia.

作者信息

Almuhawas Fida Abdulaziz, Hagr Abdulrahman Abdullah

机构信息

Dr. Abdulrahman Abdullah Hagr, Department of ORL,, King Abdulaziz University Hospital,, PO Box 245, Riyadh 11411,, Saudi Arabia, T: +966-505216261, F: +966-11-4775735,

出版信息

Ann Saudi Med. 2014 Mar-Apr;34(2):167-70. doi: 10.5144/0256-4947.2014.167.

Abstract

We present the first-published cochlear implant in an adolescent with sickle cell anemia (SCA) and bilateral profound sensorineural hearing loss (SNHL). A 15-year-old Saudi girl, previously diagnosed with SCA, developed gradual bilateral permanent profound SNHL over 18 months and underwent a successful cochlear implantation. SNHL associated with sickle cell crises is a well-known phenomenon. Regular hearing assessments are recommended for sickle cell patients, and early referrals for cochlear implantations are advocated for those with permanent profound SNHL.

摘要

我们首次报道了一名患有镰状细胞贫血(SCA)且双侧严重感音神经性听力损失(SNHL)的青少年接受人工耳蜗植入的病例。一名15岁的沙特女孩,之前被诊断为SCA,在18个月内逐渐出现双侧永久性严重SNHL,并成功接受了人工耳蜗植入。与镰状细胞危象相关的SNHL是一种众所周知的现象。建议对镰状细胞病患者进行定期听力评估,对于患有永久性严重SNHL的患者,提倡早期转诊进行人工耳蜗植入。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a4f9/6074851/99d6cbae6ad8/asm-2-167f1.jpg

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