Khan Hadi Mohammad, Katz Steven C, Libbey N Peter, Somasundar Ponnandai S
Department of Surgery, Roger Williams Medical Center, Providence, Rhode Island, USA.
Department of Pathology, Roger Williams Medical Center, Providence, Rhode Island, USA.
BMJ Case Rep. 2014 Jun 6;2014:bcr2014204122. doi: 10.1136/bcr-2014-204122.
Perivascular epithelioid cell tumour (PEComa) of the liver is very uncommon and may be overlooked in the clinical and histological differential diagnosis of a liver tumour. We report the case of an incidentally discovered liver mass suspicious for hepatocellular carcinoma, which on biopsy was suggestive of a pseudocyst but after resection was found to be hepatic PEComa with some of the usual characteristics of this neoplasm as well as several less familiar features. We have also reviewed cases of hepatic PEComa from the literature in order to provide insight into recognising possible PEComa preoperatively and assessing its risk of malignancy after diagnosis.
肝脏血管周上皮样细胞肿瘤(PEComa)非常罕见,在肝脏肿瘤的临床和组织学鉴别诊断中可能被忽视。我们报告了一例偶然发现的肝脏肿物,怀疑为肝细胞癌,活检提示为假性囊肿,但切除后发现是肝脏PEComa,具有该肿瘤的一些常见特征以及一些不太常见的特征。我们还回顾了文献中的肝脏PEComa病例,以便深入了解术前识别可能的PEComa并评估其诊断后恶性肿瘤的风险。