Gil-Julio Hernani, Vázquez-Alonso Fernando, Puche-Sanz Ignacio, Fernández-Sánchez Antonio J, Cózar-Olmo José M
Department of Urology, Virgen de las Nieves Universitary Hospital, Granada, Spain.
Curr Urol. 2012 May;6(1):46-9. doi: 10.1159/000338870. Epub 2012 Apr 30.
Primary renal malignant fibrous histiocytoma is an extremely rare disease. There are neither clinical nor radiological signs to distinguish it from the most common renal cell carcinoma. Its prognosis is poor because of its tendency to locally recur and metastasize. Therefore, early diagnosis and proper treatment are very important. We present the case of a 66-year-old woman diagnosed with primary renal malignant fibrous histiocytoma who underwent partial nephrectomy. After 41 months' follow-up, there was no evidence of any recurrence. To our knowledge, this is the first reported case of conservative surgery for this kind of tumor.
原发性肾恶性纤维组织细胞瘤是一种极为罕见的疾病。无论是临床症状还是影像学表现,均无法将其与最常见的肾细胞癌区分开来。由于其易于局部复发和转移,其预后较差。因此,早期诊断和恰当治疗非常重要。我们报告一例66岁女性原发性肾恶性纤维组织细胞瘤患者,该患者接受了部分肾切除术。经过41个月的随访,未发现任何复发迹象。据我们所知,这是首例报道的针对此类肿瘤的保守性手术病例。