Unlü Cağdaş, van den Heuvel Danyel A F, Leeuwis Jan Willem, de Vries Jean-Paul P M
Department of Vascular Surgery, St. Antonius Hospital, Nieuwegein, The Netherlands.
Department of Radiology, St. Antonius Hospital, Nieuwegein, The Netherlands.
Ann Vasc Surg. 2014 Oct;28(7):1799.e15-8. doi: 10.1016/j.avsg.2014.05.016. Epub 2014 Jun 11.
Rupture of a splenic artery aneurysm is a rare event associated with high mortality rates. Aneurysm of the splenic artery associated with fibromuscular dysplasia (FMD) is even rarer, with only 3 previously reported cases. We report a patient with previously undiagnosed FMD who required emergent intervention because of a ruptured splenic aneurysm. In discussion, we present an overview of literature on splenic aneurysms and FMD, together with pathology and treatment.
脾动脉动脉瘤破裂是一种罕见事件,死亡率很高。与纤维肌发育不良(FMD)相关的脾动脉瘤更为罕见,此前仅有3例报道。我们报告1例先前未诊断出FMD的患者,因脾动脉瘤破裂而需要紧急干预。在讨论中,我们概述了关于脾动脉瘤和FMD的文献,以及病理学和治疗方法。