婴儿期以孤立性纵隔肿块为表现的朗格汉斯细胞组织细胞增多症。
Langerhans cell histiocytosis presenting as isolated mediastinal mass in an infant.
作者信息
Ramzan Mohammed, Yadav Satya Prakash
机构信息
Pediatric Hematology Oncology and BMT Unit, Department of Pediatrics, Fortis Memorial Research Institute, Gurgaon, Haryana, India. Correspondence to: Dr Satya P Yadav, Department of Pediatrics, Fortis Memorial Research Institute, Gurgaon, Haryana, India.
出版信息
Indian Pediatr. 2014 May;51(5):397-8. doi: 10.1007/s13312-014-0405-0.
BACKGROUND
Isolated mediastinal involvement in Langerhans cell histiocytosis (LCH) has been rarely reported.
CASE CHARACTERISTICS
A 3-month-old boy presented with history of low grade intermittent fever, cough and noisy breathing for 2 weeks.
OBSERVATION
A chest X-ray showed massive mediastinal widening. Biopsy of the mass confirmed LCH.
OUTCOME
Patient is doing well after one year of treatment with LCH III protocol.
MESSAGE
Langerhans cell histiocytosis should be considered in differential diagnosis of mediastinal mass in infants.
背景
朗格汉斯细胞组织细胞增多症（LCH）孤立性纵隔受累鲜有报道。
病例特征
一名3个月大男孩，有2周低热间歇性发热、咳嗽及呼吸声粗的病史。
观察结果
胸部X线显示纵隔明显增宽。肿块活检确诊为LCH。
转归
采用LCH III方案治疗一年后患者情况良好。
启示
婴儿纵隔肿块的鉴别诊断应考虑朗格汉斯细胞组织细胞增多症。
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