Stensby J D, Conces M R, Nacey N C
Department of Radiology, University of Virginia, PO Box 800170, Charlottesville, VA, 22908, USA.
Skeletal Radiol. 2014 Nov;43(11):1639-43. doi: 10.1007/s00256-014-1940-4. Epub 2014 Jun 27.
Fibrous hamartoma of infancy is a rare fibrous tumor of the subcutaneous tissue in infants. While most case reports focus on the unique histologic appearance, which has traditionally been relied upon for diagnosis, there are few reports in the radiology literature of its appearance at MR imaging. In this report, the authors present the case of a 9-month-old male who presented with a soft tissue mass on the shoulder. The MRI findings in benign fibrous hamartoma of infancy parallel the three components of the lesion seen histologically, with an organized arrangement of fat interspersed among heterogeneous soft tissue bands composed of mesenchymal and fibrous tissue. When present, this characteristic appearance may allow the diagnosis to be suggested preoperatively.
婴儿纤维性错构瘤是一种罕见的婴儿皮下组织纤维性肿瘤。虽然大多数病例报告关注的是独特的组织学表现(传统上依靠其进行诊断),但放射学文献中关于其磁共振成像表现的报道很少。在本报告中,作者介绍了一名9个月大男性患儿的病例,该患儿肩部出现软组织肿块。婴儿良性纤维性错构瘤的磁共振成像表现与组织学上所见病变的三个组成部分相似,脂肪呈有序排列,散布于由间充质和纤维组织构成的异质性软组织带之间。如果出现这种特征性表现,可能有助于术前作出诊断。