血管性血友病因子与血管性血友病：一种复杂的蛋白质与一种复杂的疾病。
Von Willebrand factor and von Willebrand's disease: a complex protein and a complex disease.
作者信息
Bona R D
机构信息
Department of Medicine, Saint Francis Hospital, Hartford, CT 06105.
出版信息
Ann Clin Lab Sci. 1989 May-Jun;19(3):184-9.
PMID:2499240
Abstract
Von Willebrand factor is a complex protein which is important in several ways for normal hemostasis. Von Willebrand's disease results when there is either a quantitative or qualitative disorder of von Willebrand factor. In this review, the structure and function of von Willebrand factor are discussed. Additionally, the current laboratory and clinical classification of von Willebrand's disease and closely related variants are outlined.
摘要
血管性血友病因子是一种复杂的蛋白质，在正常止血的多个方面发挥着重要作用。当血管性血友病因子出现数量或质量异常时，就会引发血管性血友病。在这篇综述中，我们将讨论血管性血友病因子的结构和功能。此外，还将概述目前血管性血友病及其密切相关变异型的实验室和临床分类。
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Von Willebrand factor and von Willebrand's disease: a complex protein and a complex disease.血管性血友病因子与血管性血友病：一种复杂的蛋白质与一种复杂的疾病。
Ann Clin Lab Sci. 1989 May-Jun;19(3):184-9.
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