一名具有隐源性肝硬化临床表现患者的肝移植：以肝泡球蚴病作为原发性肝脏疾病的病例报告
Liver transplantation in a patient with clinical manifestations of cryptogenic cirrhosis: a case report of hepar lobatum as a primary liver condition.
作者信息
Bonfitto J F L, Mattosinho T J A P, Neves I, Ataide E C, Boin I F S F, Stucchi R S B, Martins D L, Escanhoela C A F
机构信息
Department of Pathology, State University of Campinas, Sao Paulo, Brazil.
Unit of Liver Transplantation, State University of Campinas, Sao Paulo, Brazil.
出版信息
Transplant Proc. 2014 Sep;46(7):2433-6. doi: 10.1016/j.transproceed.2013.09.057. Epub 2014 Jul 3.
BACKGROUND
This article reports a case of hepar lobatum, a peculiar and rare type of liver deformity, originally described in association with infectious or parasitic diseases and with malignancies.
CASE REPORT
We have described a 42-year-old woman with this disorder, which was unrelated to the known conditions and referred for liver transplantation for having clinical manifestations of cirrhosis, portal hypertension, and impaired hepatic function.
CONCLUSIONS
The observed histologic pattern suggests that hepar lobatum could be, in some patients, the effect of a primary process of hamartomatous origin involving the organ vascular supply.
背景
本文报道了一例分叶状肝，这是一种特殊且罕见的肝脏畸形类型，最初被描述与感染性或寄生虫疾病以及恶性肿瘤有关。
病例报告
我们描述了一名患有这种疾病的42岁女性，该疾病与已知疾病无关，因出现肝硬化、门静脉高压和肝功能受损的临床表现而被转诊进行肝移植。
结论
观察到的组织学模式表明，在某些患者中，分叶状肝可能是涉及器官血管供应的错构瘤起源原发性过程的结果。
Zotero 插件