Li Bin, Flaveny Colin A, Giambelli Camilla, Fei Dennis Liang, Han Lu, Hang Brian I, Bai Feng, Pei Xin-Hai, Nose Vania, Burlingame Oname, Capobianco Anthony J, Orton Darren, Lee Ethan, Robbins David J
Molecular Oncology Program, Department of Surgery, University of Miami, Miami, Florida, United States of America.
Department of Cell and Developmental Biology, Vanderbilt University School of Medicine, Nashville, Tennessee, United States of America.
PLoS One. 2014 Jul 8;9(7):e101969. doi: 10.1371/journal.pone.0101969. eCollection 2014.
Mutations in the WNT-pathway regulator ADENOMATOUS POLYPOSIS COLI (APC) promote aberrant activation of the WNT pathway that is responsible for APC-associated diseases such as Familial Adenomatous Polyposis (FAP) and 85% of spontaneous colorectal cancers (CRC). FAP is characterized by multiple intestinal adenomas, which inexorably result in CRC. Surprisingly, given their common occurrence, there are few effective chemotherapeutic drugs for FAP. Here we show that the FDA-approved, anti-helminthic drug Pyrvinium attenuates the growth of WNT-dependent CRC cells and does so via activation of CK1α. Furthermore, we show that Pyrvinium can function as an in vivo inhibitor of WNT-signaling and polyposis in a mouse model of FAP: APCmin mice. Oral administration of Pyrvinium, a CK1α agonist, attenuated the levels of WNT-driven biomarkers and inhibited adenoma formation in APCmin mice. Considering its well-documented safe use for treating enterobiasis in humans, our findings suggest that Pyrvinium could be repurposed for the clinical treatment of APC-associated polyposes.
WNT信号通路调节因子腺瘤性息肉病基因(APC)的突变会促进WNT信号通路的异常激活,而该通路与APC相关疾病有关,如家族性腺瘤性息肉病(FAP)以及85%的散发性结直肠癌(CRC)。FAP的特征是多发性肠道腺瘤,最终必然会发展为结直肠癌。令人惊讶的是,尽管这些疾病很常见,但针对FAP的有效化疗药物却很少。在这里,我们表明,美国食品药品监督管理局(FDA)批准的抗蠕虫药物吡维铵可通过激活CK1α来减弱WNT依赖性结直肠癌细胞的生长。此外,我们还表明,在FAP小鼠模型(APCmin小鼠)中,吡维铵可作为WNT信号传导和息肉病的体内抑制剂:口服CK1α激动剂吡维铵可降低WNT驱动的生物标志物水平,并抑制APCmin小鼠的腺瘤形成。鉴于其在治疗人类蛲虫病方面有充分记录的安全使用情况,我们的研究结果表明,吡维铵可重新用于APC相关息肉病的临床治疗。