Department of Neurosurgery, Adana Numune Training and Research Hospital, Adana, Turkey.
Balkan Med J. 2013 Dec;30(4):432-5. doi: 10.5152/balkanmedj.2013.8565. Epub 2013 Sep 27.
Dyke-Davidoff-Masson Syndrome (DDMS) is a rarely seen clinical entity which is characterised by cerebral hemiatrophy, contralateral hemiparesis and epilepsy. Radiological features are typical, such as unilateral atrophy of the cerebral hemisphere and associated compensatory bone changes in the skull, like thickening, enlargement of the paranasal sinuses and mastoid air cells.
In this article, we report the first case of DDMS associated with epidermoid tumour and arachnoid cyst, who underwent operation for an epidermoid tumour in the inter-hemispheric region. To our knowledge, this is the first report of DDMS associated with multiple intracranial pathologies and this association has not been previously described in the literature.
Any patient who receives DDMS in the light of clinical and radiological findings should be investigated for concomitant pathologies. Different sequences of MRI may be useful in the diagnosis of other intracranial lesions.
Dyke-Davidoff-Masson 综合征（DDMS）是一种罕见的临床实体，其特征为大脑偏侧萎缩、对侧偏瘫和癫痫。影像学特征典型，如单侧大脑半球萎缩和颅骨相关的代偿性骨改变，如鼻窦和乳突气房增厚、增大。
本文报道首例与表皮样肿瘤和蛛网膜囊肿相关的 DDMS 患者，该患者因大脑半球间的表皮样肿瘤而行手术治疗。据我们所知，这是首例报道的与多种颅内病变相关的 DDMS，且这种关联在文献中尚未有描述。
任何根据临床和影像学检查结果诊断为 DDMS 的患者均应进行伴随病变的检查。不同的 MRI 序列可能有助于颅内其他病变的诊断。
