Kühn F, Dieterich M, Klar E, Gerber B, Prinz C
Chirurgische Klinik und Poliklinik, Universität Rostock, Rostock, Germany.
Universitätsfrauenklinik und Poliklinik, Universität Rostock, Rostock, Germany.
Geburtshilfe Frauenheilkd. 2012 Aug;72(8):740-743. doi: 10.1055/s-0032-1315006.
With fewer than 250 cases published worldwide, primary vaginal melanoma is an extremely rare malignant entity which is mostly diagnosed in advanced stages. The estimated incidence of vaginal melanoma is 0.026/100 000 women per year. The poor prognosis for advanced tumour stages and different therapies used in very limited numbers of patients require precise preoperative staging and a planned interdisciplinary therapeutic approach.
原发性阴道黑色素瘤在全球范围内发表的病例少于250例,是一种极其罕见的恶性肿瘤,大多在晚期被诊断出来。阴道黑色素瘤的估计发病率为每年0.026/10万女性。晚期肿瘤阶段预后较差,且仅在极少数患者中使用了不同的治疗方法,这就需要精确的术前分期和有计划的多学科治疗方法。