原发性和转移性肾血管外皮细胞瘤。
Primary and metastatic renal hemangiopericytoma.
作者信息
Martín Martín Sergio, Torrecilla Garcia-Ripoll Juan Ramón, Trueba Arguiñarena Francisco Javier, Cortiñas Gonzalez Jose Ramon
机构信息
Urology Department. Hospital Clínico Universitario Valladolid. Spain.
出版信息
Arch Esp Urol. 2014 Oct;67(8):704-7.
OBJECTIVE
Haemangiopericytoma is an uncommon perivascular tumor that occurs more frequently in soft tissues and is extremely rare in the kidney.
METHODS
We report two cases: The first one is the case of a 57-year-old man with bilateral metastatic renal haemangiopericytoma which appeared 18 years after removal of a meningeal haemangiopericytoma. The second is a 29-year-old woman with a primary kidney haemangiopericytoma that was casually found in a nephrectomy piece.
RESULTS
In the first case, radical left nephrectomy and right renal mass radiofrequency ablation were performed. The patient had an uneventful postoperatory recovery. He remained disease-free 22 months after surgery but two new lesions appeared that were treated with radiofrequency ablation. The second case was a casual finding, a small tumor that had been totally resected.
CONCLUSIONS
Haemangiopericytoma is a rare tumor with an uncertain clinical behaviour. Long-term follow up is important as local recurrences and metastases can develop years after initial treatment.
目的
血管外皮细胞瘤是一种罕见的血管周围肿瘤，多见于软组织，在肾脏极为罕见。
方法
我们报告两例病例：第一例是一名57岁男性，患有双侧转移性肾血管外皮细胞瘤，在脑膜血管外皮细胞瘤切除18年后出现。第二例是一名29岁女性，在肾切除标本中偶然发现原发性肾血管外皮细胞瘤。
结果
第一例病例中，实施了左肾根治性切除术和右肾肿物射频消融术。患者术后恢复顺利。术后22个月时无疾病复发，但出现了两个新病灶，接受了射频消融治疗。第二例病例是偶然发现的，一个小肿瘤已被完全切除。
结论
血管外皮细胞瘤是一种临床行为不确定的罕见肿瘤。由于局部复发和转移可能在初始治疗数年之后出现，因此长期随访很重要。
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