Carcamo Valor P, Martínez-Piñeiro J A, López-Tello J, Picazo García M, Contreras Rubio F
Servicio de Urología, Hospital La Paz, Facultad de Medicina, Universidad Autónoma, Madrid, España.
Arch Esp Urol. 1996 Nov;49(9):944-9.
Since the initial report of renal hemangiopericytoma by Black and Heinemann in 1955, only 24 cases of this rare vascular neoplasm, involving the renal capsule, parenchyma or sinus have been described in the world literature. Herein we describe an additional case and review the literature.
We report on a 65-old woman in whom a 5 x 4 cm solid mass was incidentally found in the left sinus. The tumor compressed the renal pelvis and caused hydronephrosis and parenchymal atrophy. A radical left nephrectomy was performed. Histological and immunological studies revealed a hemangiopericytoma of renal sinus soft tissues.
The patient did well postoperatively and remains disease-free at the present time.
Although there are other histological and clinical criteria indicative of worse prognosis, the malignancy of hemangiopericytoma is determined by the presence of hematogenous metastases.
自1955年布莱克和海涅曼首次报告肾血管外皮细胞瘤以来，世界文献中仅描述了24例这种罕见的血管性肿瘤，累及肾包膜、实质或肾窦。在此，我们描述另外1例病例并回顾相关文献。
我们报告了1例65岁女性，其左肾窦偶然发现一个5×4cm的实性肿块。肿瘤压迫肾盂，导致肾积水和实质萎缩。实施了根治性左肾切除术。组织学和免疫学研究显示为肾窦软组织血管外皮细胞瘤。
患者术后恢复良好，目前无疾病复发。
尽管还有其他组织学和临床标准提示预后较差，但血管外皮细胞瘤的恶性程度取决于是否存在血行转移。
