Mirza Bilal, Ahmad Sarfraz, Wasti Arsalan Raza, Mirza Muhammad Afzal, Talat Nabila, Saleem Muhammad
Department of Paediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore, Pakistan.
Afr J Paediatr Surg. 2014 Oct-Dec;11(4):326-9. doi: 10.4103/0189-6725.143143.
Classical duplications may present along any part of gastrointestinal tract (GIT) from mouth to anus. Atypical or unusual rare varieties of GIT duplications may also occur, but with different anatomical features.
We reviewed our 5-year record (February 2008-January 2013) to describe clinical profile of unusual GIT duplications in neonates and small infants.
Three patients with atypical variety of GIT duplications were managed in our department during this tenure. Two were females and one male. Age was ranged between 11 days and 2 months. All patients presented with massive abdominal distension causing respiratory embarrassment in two of them. In all patients, the pre-operative differential diagnoses also included GIT duplication cysts. Computerized tomography (CT) scan showed single huge cyst in one and multiple cysts in two patients. In one patient the CT scan also depicted a thoracic cyst in relation to posterior mediastinum. At operation, one patient had colonic tubular duplication cyst along with another isolated duplication cyst, the second case had a tubular duplication cyst of ileum with its segmental dilatation, and in the third case two isolated duplications were found. Duplication cysts were excised along with mucosal stripping in one patient, cyst excision and intestinal resection and anastomosis in one patient, and only cysts excision in one. All patients did well post-operatively.
We presented unusual GIT duplications. These duplications are managed on similar lines as classical duplications with good prognosis when dealt early.
经典型消化道重复畸形可出现在从口腔到肛门的胃肠道(GIT)的任何部位。非典型或罕见的消化道重复畸形也可能发生,但具有不同的解剖特征。
我们回顾了我们5年的记录(2008年2月至2013年1月),以描述新生儿和小婴儿非典型消化道重复畸形的临床特征。
在这段时间里,我们科室收治了3例非典型消化道重复畸形患者。2例为女性,1例为男性。年龄在11天至2个月之间。所有患者均出现严重腹胀,其中2例导致呼吸窘迫。所有患者术前的鉴别诊断还包括消化道重复畸形囊肿。计算机断层扫描(CT)显示1例为单个巨大囊肿,2例为多个囊肿。1例患者的CT扫描还显示与后纵隔相关的胸段囊肿。手术中,1例患者有结肠管状重复畸形囊肿以及另一个孤立的重复畸形囊肿,第2例患者有回肠管状重复畸形囊肿及其节段性扩张,第3例患者发现两个孤立的重复畸形。1例患者切除重复畸形囊肿并进行黏膜剥脱,1例患者进行囊肿切除、肠切除和吻合,1例仅进行囊肿切除。所有患者术后恢复良好。
我们报告了非典型消化道重复畸形。这些重复畸形的治疗方法与经典型重复畸形相似,早期治疗预后良好。