Iyer C P, Mahour G H
Division of Pediatric Surgery, Children's Hospital Los Angeles, CA 90027, USA.
J Pediatr Surg. 1995 Sep;30(9):1267-70. doi: 10.1016/0022-3468(95)90482-4.
Duplications of the alimentary tract are rare congenital anomalies that could present a diagnostic as well as therapeutic challenge. Twenty-seven patients with duplications of the alimentary tract were treated at Childrens Hospital Los Angeles between 1961 and 1992. Ages ranged from a few days to 5 years (67% younger than 1 year). The most common symptoms were nausea and vomiting, and the most common sign was a palpable abdominal mass. Three patients presented with gastric duplication, which was excised. The majority of the duplications were in the jejunum and ileum. All patients except one had primary resection of the duplication. One patient with a 45-cm tubular jejunal duplication was treated with mucosal stripping of the duplication. Five patients had cecal duplication, three patients presented with melena because of ectopic gastric tissue in the duplication, and two presented with intestinal obstruction. One of the latter patients presented with intussusception with cecal duplication as the leading point. Three patients with colonic duplication presented with abdominal pain and vomiting leading to excision of the duplication. Of the five patients with rectal duplication, three presented with chronic constipation. The other two patients presented elsewhere with perianal swelling, which eventually was drained because of a mistaken diagnosis of perianal abscess. Subsequently, these two patients came to us with persistent perineal fistula. In all our patients, rectal duplications were removed through a sacroperineal incision. The only patient in this series who died was a 6-week-old boy with gastric duplication; his death was attributed to an associated severe cardiac lesion.(ABSTRACT TRUNCATED AT 250 WORDS)
消化道重复畸形是罕见的先天性异常,会带来诊断和治疗方面的挑战。1961年至1992年间,洛杉矶儿童医院共治疗了27例消化道重复畸形患者。年龄从几天到5岁不等(67%小于1岁)。最常见的症状是恶心和呕吐,最常见的体征是可触及的腹部肿块。3例患者出现胃重复畸形,均接受了切除手术。大多数重复畸形位于空肠和回肠。除1例患者外,所有患者均接受了重复畸形的一期切除。1例患有45厘米管状空肠重复畸形的患者接受了重复畸形黏膜剥脱术治疗。5例患者有盲肠重复畸形,3例因重复畸形内异位胃组织出现黑便,2例出现肠梗阻。其中1例患者以盲肠重复畸形为套叠起点出现肠套叠。3例结肠重复畸形患者出现腹痛和呕吐,最终接受了重复畸形切除术。5例直肠重复畸形患者中,3例出现慢性便秘。另外2例患者在其他地方出现肛周肿胀,最终因误诊为肛周脓肿而进行了引流。随后,这2例患者因持续性会阴瘘前来我院就诊。在我们所有的患者中,直肠重复畸形均通过骶会阴切口切除。本系列中唯一死亡的患者是一名6周大患有胃重复畸形的男孩,其死亡归因于相关的严重心脏病变。(摘要截选至250字)