Terada Takafumi, Sakurai Hajime, Nonaka Toshimichi, Sakurai Takahisa, Sugiura Junya, Otsuka Ryohei
Department of Cardiovascular Surgery, Chukyo Hospital, Aichi, Japan
Department of Cardiovascular Surgery, Chukyo Hospital, Aichi, Japan.
World J Pediatr Congenit Heart Surg. 2014 Oct;5(4):583-5. doi: 10.1177/2150135114542164.
Aortico-left ventricular tunnel (ALVT) is a rare congenital anomaly presenting abnormal connection between the ascending aorta and the left ventricle. In most reported cases, the aortic end of the tunnel is above the right coronary sinus. Cases of ALVT related to the left aortic sinus are extremely rare. We herein report a case diagnosed preoperatively as ALVT arising from the left aortic sinus. The actual diagnosis observed at surgery was aortic valve insufficiency with a left ventricular outflow tract aneurysm. We successfully performed aortic valve repair and plication of the left ventricular aneurysm.
主动脉-左心室通道（ALVT）是一种罕见的先天性异常，表现为升主动脉与左心室之间的异常连接。在大多数报道的病例中，通道的主动脉端位于右冠状动脉窦上方。与左主动脉窦相关的ALVT病例极为罕见。我们在此报告一例术前诊断为起源于左主动脉窦的ALVT病例。手术中实际观察到的诊断是主动脉瓣关闭不全合并左心室流出道动脉瘤。我们成功地进行了主动脉瓣修复和左心室动脉瘤折叠术。
