Emori M, Kaya M, Sugita S, Soma T, Sasaki M, Yamashita T
Sapporo Medical University, Japan.
Ann R Coll Surg Engl. 2014 Nov;96(8):e8-11. doi: 10.1308/003588414X13946184902686.
Chordomas are rare, low grade, malignant tumours derived from the ectopic remnants of the notochord that line the axial skeleton. They are characterised by their slow growth, long disease course and propensity for local relapse. Furthermore, up to 40% of non-cranial chordomas metastasise. We describe the first reported case of a hand metastasis arising from a conventional sacral chordoma after carbon ion radiotherapy. The common occurrence of distant metastasis with chordomas makes it important to perform a systemic examination, in part because their resection might improve patient prognosis.
脊索瘤是一种罕见的、低级别恶性肿瘤,起源于沿中轴骨骼分布的脊索异位残余组织。其特点是生长缓慢、病程长且易于局部复发。此外,高达40%的非颅部脊索瘤会发生转移。我们报告了首例经碳离子放疗后,常规骶骨脊索瘤发生手部转移的病例。脊索瘤常见远处转移,因此进行全身检查很重要,部分原因是切除肿瘤可能改善患者预后。