Harada Kenichi, Ichikawa Daisuke, Konishi Hirotaka, Komatsu Shuhei, Shiozaki Atsushi, Fujiwara Hitoshi, Okamoto Kazuma, Otsuji Eigo
Division of Digestive Surgery, Department of Surgery, Kyoto Prefectural University of Medicine, Kyoto, Japan.
Int Surg. 2014 Nov-Dec;99(6):685-90. doi: 10.9738/INTSURG-D-14-00058.1.
Amyloidosis is a metabolic disease that results in organ dysfunction because of the deposition of amyloid proteins in body tissues and organs. Amyloid accumulation in the gastrointestinal tract can lead to severe complications with poor outcomes. We report a case showing simultaneous perforation of the sigmoid colon and massive segmental intestinal ischemia caused by amyloidosis associated with multiple myeloma. A 75-year-old woman presented to the emergency department in our hospital with a chief complaint of abdominal pain. Results of several examinations indicated sigmoid colon perforation and acute generalized peritonitis. She underwent an emergency exploratory laparotomy. Operative finding was a perforation of the sigmoid colon and many segmental discoloration sites appeared intraoperatively in the small intestine. A loop colostomy was performed by employing a double-barrel ileostomy with a massive resection of the segmentally discolored small bowel. Pathological findings suggested that the causative factor was amyloidosis with multiple myeloma. The patient was successfully treated with adequate surgery and with melphalan and prednisone after the operation. Meticulous and appropriate treatment for severe complications involving amyloidosis associated with multiple myeloma can prevent a fatal outcome.
淀粉样变性是一种代谢性疾病,由于淀粉样蛋白在身体组织和器官中的沉积而导致器官功能障碍。胃肠道中的淀粉样蛋白积累可导致严重并发症,预后不良。我们报告一例病例,显示由与多发性骨髓瘤相关的淀粉样变性引起的乙状结肠同时穿孔和大面积节段性肠缺血。一名75岁女性因腹痛为主诉就诊于我院急诊科。多项检查结果提示乙状结肠穿孔和急性弥漫性腹膜炎。她接受了急诊剖腹探查术。手术发现乙状结肠穿孔,术中小肠出现多处节段性变色部位。采用双腔回肠造口术并大量切除节段性变色的小肠进行了袢式结肠造口术。病理结果提示病因是伴有多发性骨髓瘤的淀粉样变性。患者术后通过适当的手术以及美法仑和泼尼松成功治愈。对涉及与多发性骨髓瘤相关的淀粉样变性的严重并发症进行细致恰当的治疗可避免致命后果。