Pallisgaard Jannik L, Gang Uffe, Kanters Jørgen K, Hansen Peter R
Department of Cardiology, Copenhagen University Hospital Gentofte, Hellerup, Denmark.
Am J Case Rep. 2014 Dec 16;15:559-61. doi: 10.12659/AJCR.892314.
Brugada syndrome (BrS) is a genetic arrhythmogenic disease characterized by ST-segment elevations in the right precordial leads of the electrocardiogram (ECG). These ECG changes may be concealed and BrS may present with electrical storm characterized by recurrent ventricular tachycardia and fibrillation.
A 49-year-old previously healthy man was admitted with electrical storm. The patient received direct current (DC) cardioversion shocks and only after intravenous lidocaine did the electrical storm slowly subside with a total of 255 DC shocks administered during the first 24 h after admission. He fully recovered and received an implantable cardioverter-defibrillator. Subsequent drug challenge with flecainide revealed type 1 BrS.
Massive electrical storm can be the first symptom of BrS and the diagnostic ECG changes may be concealed at presentation. Although hundreds of DC shocks may be required during initial treatment, full recovery can be achieved.
Brugada综合征（BrS）是一种遗传性致心律失常疾病，其特征为心电图（ECG）右胸前导联ST段抬高。这些心电图改变可能是隐匿性的，BrS可能表现为以反复室性心动过速和颤动为特征的电风暴。
一名49岁既往健康的男性因电风暴入院。患者接受了直流电（DC）复律电击，仅在静脉注射利多卡因后，电风暴才逐渐平息，入院后最初24小时内共进行了255次DC电击。他完全康复并接受了植入式心脏复律除颤器。随后用氟卡尼进行药物激发试验显示为1型BrS。
大规模电风暴可能是BrS的首发症状，诊断性心电图改变在发病时可能是隐匿的。虽然初始治疗期间可能需要数百次DC电击，但仍可实现完全康复。
