Juaneda Ignacio, Rychik Jack, Fuller Stephanie, Weinberg Paul M, Rome Jonathan J, Mahle William T, Gaynor J William
Division of Pediatric Cardiothoracic Surgery, The Children's Hospital of Philadelphia, PA, USA
Division of Pediatric Cardiology, The Children's Hospital of Philadelphia, Perelman School of Medicine at The University of Pennsylvania, Philadelphia, PA, USA.
World J Pediatr Congenit Heart Surg. 2015 Jan;6(1):98-100. doi: 10.1177/2150135114544752.
We describe management of a patient with a prenatal diagnosis of absent pulmonary valve, tricuspid atresia, ventricular septal defect, and congenital heart block. Initial treatment consisted of temporary pacemaker implantation, and subsequent palliation included a central shunt during the neonatal period and placement of a permanent pacemaker. At seven months of age, a bidirectional Glenn anastomosis was performed. Cardiac catheterization revealed high cavopulmonary pressures and ventricular dysfunction precluding Fontan completion. Heart transplantation was performed at 3.75 years of age. The patient is alive and well 26 months posttransplantation.
我们描述了一名产前诊断为肺动脉瓣缺如、三尖瓣闭锁、室间隔缺损和先天性心脏传导阻滞患者的治疗情况。初始治疗包括植入临时起搏器，随后的姑息治疗包括在新生儿期进行中心分流术以及植入永久性起搏器。在7个月大时，进行了双向格林吻合术。心导管检查显示腔肺压力高和心室功能障碍，无法完成Fontan手术。患者在3.75岁时接受了心脏移植。移植后26个月，患者存活且状况良好。
