Shetty Ravi Shankar, Thareen Jameel Khan, Ramaiah Anil Kumar Hpalya, Narayan Ravi, Das Jayantha Kumar, Chandrashekariah Mahesh M
Department of Cardiothoracic Surgery, MS Ramaiah Narayana Heart Center, MS Ramaiah Memorial Hospital, Bangalore, Karnataka, India.
Department of Cardiothoracic Anesthesiology, MS Ramaiah Narayana Heart Center, MS Ramaiah Memorial Hospital, Bangalore, Karnataka, India
World J Pediatr Congenit Heart Surg. 2015 Jan;6(1):108-10. doi: 10.1177/2150135114551030.
Anomalous origin of a single coronary artery from the pulmonary artery is a rare and potentially fatal congenital heart malformation. Although the actual incidence is not known, it is rarer than anomalous left coronary artery from pulmonary artery. In the absence of other important congenital cardiac anomalies, patients with anomalous origin of a single coronary artery from the pulmonary artery typically experience myocardial ischemia in association with the physiological decrease in the pulmonary vascular resistance that typically occurs over the first few months of life. To our knowledge, there have been only three reported cases of successful surgical correction. We describe a very unusual case in which the diagnosis was made intraoperatively during surgery to close a ventricular septal defect.
单一冠状动脉起源于肺动脉是一种罕见且可能致命的先天性心脏畸形。虽然实际发病率尚不清楚，但它比左冠状动脉起源于肺动脉更为罕见。在没有其他重要先天性心脏异常的情况下，单一冠状动脉起源于肺动脉的患者通常会在出生后的头几个月内，随着肺血管阻力的生理性下降而出现心肌缺血。据我们所知，仅有3例成功手术矫正的报道病例。我们描述了一个非常特殊的病例，该病例是在手术闭合室间隔缺损时术中确诊的。
