Liu Zhe, Xu Yuanhong, Long Jin, Guo Kejian, Du Ruixia
Department of Pancreatic Surgery, First Hospital of China Medical University Shenyang, China.
Department of Otorhinolaryngology, Fengtian Hospital, Shenyang Medical University Shenyang, China.
Int J Clin Exp Med. 2014 Nov 15;7(11):4526-9. eCollection 2014.
Retroperitoneal liposarcoma (RPLS) is a rare malignant tumor yet with a high recurrence rate. It is mostly observed in limbs and during retroperitoneal clearance, and accounts for nearly 40% of all adult retroperitoneal soft tissue sarcomas [1]. Renal cell carcinoma (RCC) is a common cancer developed in urinary system and its occurrence rate accounts for 3% of whole body malignant tumors [2]. In this report, we present a case of large perirenal liposarcoma associated with RCC, which is to date the fourth identified case. We analyzed the clinical pathologic data of this patient and reviewed the other three cases. Compared to the other cases, this patient is diagnosed at the youngest age and the liposarcoma tumor is with the largest diameter. Moreover, we have been following up the patient after operation for the longest time. All of these made this report rare and important.
腹膜后脂肪肉瘤（RPLS）是一种罕见的恶性肿瘤，但复发率很高。它大多发生于四肢以及腹膜后清除术中，占所有成人腹膜后软组织肉瘤的近40%[1]。肾细胞癌（RCC）是泌尿系统常见的癌症，其发生率占全身恶性肿瘤的3%[2]。在本报告中，我们呈现了一例与肾细胞癌相关的巨大肾周脂肪肉瘤病例，这是迄今为止第四例确诊病例。我们分析了该患者的临床病理资料，并回顾了其他三例病例。与其他病例相比，该患者确诊时年龄最小，脂肪肉瘤肿瘤直径最大。此外，我们对该患者术后的随访时间最长。所有这些使得本报告既罕见又重要。
