Crisan Nicolae, Ivan Cristina S, Bungardean Catalina, Cebotaru Cristina, Coman Ioan
Urology Department, Cluj-Napoca County Hospital, Cluj Napoca, Romania.
Urology Department, Cluj-Napoca County Hospital, Cluj Napoca, Romania
J Surg Case Rep. 2015 Mar 5;2015(3):rju127. doi: 10.1093/jscr/rju127.
Liposarcomas are neoplasms of mesodermic origin, are derived from adipose tissue and represent <1% of all malignant tumours. Primary liposarcomas of the kidney are very rare. Here, we present the cases of two patients diagnosed with retroperitoneal perirenal myxoid liposarcoma. The patients were diagnosed via imaging, which in both cases revealed a huge right retroperitoneal tumour mass compressing the abdominal organs and large blood vessels. Surgical intervention consisting of en bloc resection of the tumour and the right kidney was performed using a transperitoneal approach. Three years after the surgery, both patients presented local recurrence, for which they underwent chemotherapy. Liposarcomas with renal origin are rare clinical entities with a high rate of malignancy and a poor prognosis. Because the use of chemotherapy and radiotherapy in the treatment of such liposarcomas is controversial, the treatment of choice is wide surgical resection with clean margins.
脂肪肉瘤是中胚层起源的肿瘤，源自脂肪组织，占所有恶性肿瘤的比例不到1%。原发性肾脂肪肉瘤非常罕见。在此，我们报告两例被诊断为腹膜后肾周黏液样脂肪肉瘤的患者病例。患者通过影像学检查确诊，两例均显示巨大的右侧腹膜后肿瘤肿块，压迫腹部器官和大血管。采用经腹入路进行了包括肿瘤和右肾整块切除的手术干预。手术后三年，两名患者均出现局部复发，并接受了化疗。肾源性脂肪肉瘤是罕见的临床实体，恶性率高且预后不良。由于化疗和放疗在这类脂肪肉瘤治疗中的应用存在争议，首选的治疗方法是进行切缘干净的广泛手术切除。
