Cabral Fernanda C, Trotman-Dickenson Beatrice, Madan Rachna
Department of Radiology, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
Department of Radiology, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
Eur J Radiol. 2015 Mar;84(3):489-498. doi: 10.1016/j.ejrad.2014.11.039. Epub 2014 Dec 15.
Hypervascular mediastinal masses are a distinct group of rare diseases that include a subset of benign and malignant entities. Characteristic features and known association with syndromes and genetic mutations assist in achieving a diagnosis. Imaging allows an understanding of the vascularity of the lesion and should alert the radiologist and clinician to potential hemorrhagic complications and avoid percutaneous CT guided biopsies. In such cases, pre-procedure embolization and surgical biopsy maybe considered for better control of post procedure hemorrhage. The purpose of this article is to describe and illustrate the clinical features and radiologic spectrum of hypervascular mediastinal masses, and discuss the associated clinical and genetic syndromes. We will present an imaging algorithm to determine further evaluation and subsequently guide treatment.
富血管性纵隔肿块是一组独特的罕见疾病,包括良性和恶性病变的一个子集。其特征性表现以及与综合征和基因突变的已知关联有助于做出诊断。影像学检查有助于了解病变的血管情况,并应提醒放射科医生和临床医生注意潜在的出血并发症,避免进行CT引导下经皮活检。在这种情况下,可考虑在术前进行栓塞和手术活检,以便更好地控制术后出血。本文旨在描述和阐述富血管性纵隔肿块的临床特征和放射学表现,并讨论相关的临床和遗传综合征。我们将提出一种影像学检查流程,以确定进一步的评估方法,进而指导治疗。