Benmansour Anis, Laanaz Saad, Bougtab Abdeslam
Department of Surgical Oncology, National Institute of Oncology, Rabat, Morocco.
Department of Medical Oncology, National Institute of Oncology, Rabat, Morocco.
Pan Afr Med J. 2014 Sep 1;19:2. doi: 10.11604/pamj.2014.19.2.4178. eCollection 2014.
The Stewart-Treves syndrome was first described in 1948, it's an angiosarcoma developed on a longstanding lymphadenomatous limb, more often after radical mastectomy. Diagnosis is made on skin biopsy and the prognosis is poor when radical surgery can't be performed. We report the case on a Stewart-Treves syndrome in a sixty-six years old woman who underwent radical mastectomy for breast carcinoma ten years earlier. Surgery was not feasible at the time of diagnosis, and we lost touch of the patient even if chemotherapy was decided. Radical surgery is the best treatment to date for this rare disease. Conservative surgery with adjuvant radiotherapy is also possible. Systemic chemotherapy is reserved for locally advanced unresectable and metastatic forms. We advocate long term follow-up for every post mastectomy lymphedema to diagnosis this fatal disease when curable.
斯图尔特 - 特里夫斯综合征于1948年首次被描述,它是一种发生在长期存在的肢体淋巴腺瘤上的血管肉瘤,更多见于根治性乳房切除术后。通过皮肤活检进行诊断,当无法进行根治性手术时预后较差。我们报告一例66岁女性的斯图尔特 - 特里夫斯综合征病例,该患者10年前因乳腺癌接受了根治性乳房切除术。诊断时手术不可行,即便决定进行化疗,我们也与患者失去了联系。根治性手术是目前治疗这种罕见疾病的最佳方法。辅助放疗的保守手术也是可行的。全身化疗适用于局部晚期不可切除和转移性病例。我们主张对每例乳房切除术后淋巴水肿进行长期随访,以便在可治愈时诊断出这种致命疾病。