Kawakami Masayoshi, Yamamoto Kazuhiko, Shimomura Tadahiro, Kirita Tadaaki
Cleft Palate Craniofac J. 2016 Mar;53(2):253-8. doi: 10.1597/14-196. Epub 2015 Jan 9.
Noonan syndrome, characterized by short stature, facial anomalies, and congenital heart defects, may also be associated with hematopoietic disorders. Craniofacial anomalies in affected patients include hypertelorism and severe open bite associated with masticatory dysfunction. We treated a Noonan syndrome patient with a skeletal open bite. Surgical orthodontic treatment including two-jaw surgery established a good occlusal relationship after correction of severe anemia. Both upper and lower incisors were moved to upright positions, while clockwise rotation of the palatal plane and decreased mandibular plane angle were accomplished. Lower masticatory activity may affect posttreatment occlusion in such cases.
努南综合征以身材矮小、面部异常和先天性心脏缺陷为特征,也可能与造血系统疾病有关。受影响患者的颅面异常包括眼距过宽和与咀嚼功能障碍相关的严重开合。我们治疗了一名患有骨性开合的努南综合征患者。包括双颌手术在内的外科正畸治疗在纠正严重贫血后建立了良好的咬合关系。上下切牙均移动到直立位置,同时完成了腭平面的顺时针旋转和下颌平面角的减小。在这种情况下,下颌咀嚼活动可能会影响治疗后的咬合。