Boulot P, Pages A, Deschamps F, Courtieu C, Jalaguier J, Hedon B, Laffargue F, Viala J L
Services de Gynécologie-Obstétrique, Centre Hospitalier et Universitaire, Faculté de Médecine, Montpellier.
J Gynecol Obstet Biol Reprod (Paris). 1989;18(8):1037-40.
The authors report a new case of the antenatal ultrasound diagnosis of a congenital mesoblastic nephroma (also called Bolande's tumor) at 33 weeks of amenorrhea. This tumor was found to be associated with acute hydramnios involving premature labor and fetal death by respiratory embarrassment. Congenital mesoblastic nephroma is a very rare entity but is the predominant renal neoplasm in the immediate neonate period. The differential diagnosis between Bolande's tumor and nephroblastoma (Wilm's tumor) is now clear since histopathological features have been precisely described by Bolande. Clinical and pathological features of the renal disease are discussed. The prognosis is excellent for most cases requiring only surgical treatment (nephrectomy).
作者报告了一例孕33周时经产前超声诊断为先天性中胚层肾瘤（也称为博兰德瘤）的新病例。发现该肿瘤与羊水过多相关，后者导致早产及胎儿因呼吸窘迫死亡。先天性中胚层肾瘤是一种非常罕见的实体瘤，但却是新生儿期最主要的肾肿瘤。由于博兰德已精确描述了其组织病理学特征，目前博兰德瘤与肾母细胞瘤（威尔姆斯瘤）之间的鉴别诊断已明确。文中讨论了该肾病的临床和病理特征。大多数病例仅需手术治疗（肾切除术），预后良好。
